Osteofibrous Dysplasia is a rare benign bone tumor that typically develops in children and adolescents. Usually, it develops in the middle of the shin (tibia), although it can also develop in the fibula and the long bones of the arm.
Osteofibrous Dysplasia makes up less than 1% of all bone tumors, typically appearing in patients under 20 years of age. The tumor develops as a child grows up, but this growth slows or stops once bone development is complete.
Osteofibrous Dysplasia is often discovered through x-rays performed to diagnose a separate issue, as in many cases, no symptoms are present to indicate the presence of the tumor. When symptoms do appear, they may include swelling or pain where the tumor is located, fractures in parts of the bone weakened by the tumor, or bowing of the leg.
There’s no clear indication of what causes Osteofibrous Dysplasia, though there is believed to be a connection between this condition and adamantinoma, another rare form of bone tumor that, unlike Osteofibrous Dysplasia, is malignant. There’s currently no evidence that Osteofibrous Dysplasia can lead to adamantinoma.
Since it’s typically benign, doctors often take a conservative approach to Osteofibrous Dysplasia treatment, usually only observing the tumor through x-rays performed every few months. If it’s causing bone fractures or bowing, a brace may be recommended to prevent further damage. In cases where the damage is more severe, however, surgery may be recommended to remove the tumor and stabilize the bone.
If Osteofibrous Dysplasia is causing injuries to your child’s bones, get help from our board-certified pediatric orthopedic specialists. Schedule a consultation with one of our doctors now.